CLASSIFICATION SYSTEM
Following is a classification system provided by Fan for ILDPediatric
ILD of Known Etiology
Aspiration
syndromes
Chronic infection in immune competent host
Chronic infection in immune incompetent host
viral
bacterial
fungal
parasitic
BPD:
Occupational, environmental and physical exposures
Hypersensitivity
pneumonitis
Drug-induced lung disease
Radiation-induced lung disease
Oxygen-toxicity-induced lung disease
Chemical fume-induced lung disease
Mineral dust-induced lung disease
Lipid storage disorders
Pediatric
ILD of Unknown Etiology
UIP
DIP
LIP and related disorders
Associated
with autoimmune disorders (Wegener's, MCTD, UC, pulmonary renal syndromes)
Associated with malignancies
Pulmonary hemosiderosis
Pulmonary histiocytosis
Pulmonary infiltrates with eosinophilia
Pulmonary vascular disorders (VOD, pulmonary hemangiomatosis, pulmonary
venous obstruction)
Sarcoidosis Bronchiolitis obliterans +/- organizing pneumonia
Alveolar proteinosis
Neurocutaneous syndromes
Cellular interstitial pneumonitis
Nonspecific interstitial lung disease (chronic pneumonitis of infancy)
